Tetralogy of Fallot is the commonest cyanotic congenital heart disease, occurring in 1 in 3600 live births.
The four features of Tetralogy of Fallot are:
- Pulmonary stenosis
- Ventricular septal defects
- Right ventricular hypertrophy
- Overriding of the aorta
Treatment is surgical repair.
Prognosis:
- 40 year survival rate at least 90%
- Complications in adulthood include
- pulmonary regurgitation (low-pitched, diastolic murmur)
- right heart failure
- arrhythmias (6% risk of sudden cardiac death)
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